Neuromuscular Disorders: A Symptoms and Signs Approach to Differential Diagnosis and Treatment

241 Pages·2017·7.94 MB·English

by  Nicholas Silvestri

Neuromuscular Disorders

Neuromuscular Disorders
A Symptoms and Signs Approach to Differential
Diagnosis and Treatment
Editor
Nicholas J. Silvestri, MD
Associate Professor of Neurology
Department of Neurology
University at Buffalo Jacobs School of Medicine & Biomedical Sciences
Buffalo, New York
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Library of Congress Cataloging-in-Publication Data
Names: Silvestri, Nicholas J., editor.
Title: Neuromuscular disorders: a symptoms and signs approach to
differential diagnosis and treatment / Nicholas J. Silvestri, editor.
Other titles: Neuromuscular disorders (Silvestri)
Description: New York: Demos Medical Publishing/Springer Publishing Company,
[2018] | Includes bibliographical references and index.
Identifi ers: LCCN 2017034196 | ISBN 9780826171986 | ISBN 9780826171993 (e-book)
Subjects: | MESH: Neuromuscular Diseases—diagnosis | Neuromuscular
Diseases—therapy
Classifi cation: LCC RC925.55 | NLM WE 550 | DDC 616.7/44—dc23
LC record available at https://lccn.loc.gov/2017034196
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Contents
Contributors ix
Foreword Gil I. Wolfe, MD xi
Preface xiii
Share Neuromuscular Disorders: A Symptoms and Signs Approach
to Differential Diagnosis and Treatment
1. Interpretation of Tests Used in Neuromuscular Disorders 1
Diana Mnatsakanova and David Lacomis
2. Acute Generalized Weakness 41
Simona Treidler and Yaacov Anziska
3. Subacutely Developing Weakness 61
Mamatha Pasnoor, Mazen M. Dimachkie, and Richard J. Barohn
4. Chronically Developing Weakness 91
Hans D. Katzberg, Ari Breiner, and Aaron Izenberg
5. Episodic Weakness and Exercise Intolerance 107
Carolina Barnett and Charles Kassardjian
6. Ocular and Bulbar Symptoms 123
Michael K. Hehir
7. Neuromuscular Respiratory Failure 145
Nicholas J. Silvestri, Karin Provost, and Daniel W. Sheehan
8. Sensory Loss and Neuropathic Pain 163
Kelly G. Gwathmey and Nora Jovanovich
9. Limb Pain 201
Andrew W. Tarulli
Index 217
vii

Contributors
Yaacov Anziska, MD, MS, Assistant Professor of Neurology, Department of
Neurology, SUNY Downstate Medical Center, Brooklyn, New York
Carolina Barnett, MD, PhD, Assistant Professor, Division of Neurology,
Department of Medicine, University Health Network, University of Toronto,
Toronto, Ontario, Canada
Richard J. Barohn, MD, Gertrude and Dewey Ziegler Professor of Neurology,
University Distinguished Professor, Vice Chancellor for Research, President,
Research Institute, University of Kansas Medical Center, Kansas City, Kansas
Ari Breiner, MD, MSc, FRCPC, Assistant Professor, Division of Neurology,
Department of Medicine, University Health Network, University of Toronto,
Toronto, Ontario, Canada
Mazen M. Dimachkie, MD, Professor of Neurology, Director, Neuromuscular
Division, Executive Vice Chairman and Vice Chairman for Research
Programs, Department of Neurology, University of Kansas Medical Center,
Kansas City, Kansas
Kelly G. Gwathmey, MD, Assistant Professor of Neurology, Department of
Neurology, University of Virginia, Charlottesville, Virginia
Michael K. Hehir, MD, Associate Professor, Division Chief, Neuromuscular
Medicine, Department of Neurosciences, Larner College of Medicine at the
University of Vermont, Burlington, Vermont
Aaron Izenberg, MD, FRCPC, Division of Neurology, Department of
Medicine, Sunnybrook Health Sciences Centre, University of Toronto,
Toronto, Ontario, Canada
Nora Jovanovich, MD, Department of Neurology, University of Virginia,
Charlottesville, Virginia
Charles Kassardjian, MD, FRCP, Division of Neurology, Department of Medicine,
St. Michael’s Hospital and University of Toronto, Toronto, Ontario, Canada
ix