Table Of ContentRespiratory Medicine
Series Editor: Sharon I.S. Rounds
Marc A. Judson Editor
Pulmonary
Sarcoidosis
A Guide for the Practicing Clinician
R espiratory Medicine
Series Editor:
Sharon I.S. Rounds
F or further volumes:
h ttp://www.springer.com/series/7665
M arc A. J udson
E ditor
P ulmonary Sarcoidosis
A Guide for the Practicing Clinician
E ditor
M arc A. J udson, M.D.
D ivision of Pulmonary
and Critical Care Medicine
Department of Medicine
A lbany Medical College
A lbany, N Y, U SA
I SBN 978-1-4614-8926-9 ISBN 978-1-4614-8927-6 (eBook)
D OI 10.1007/978-1-4614-8927-6
S pringer New York Heidelberg Dordrecht London
L ibrary of Congress Control Number: 2013949139
© Springer Science+Business Media New York 2 014
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T his book is dedicated to Sooyeon Kwon,
my beautiful, loving, and intelligent wife.
Her caring and support has made many
things possible in my life, including this work.
P refa ce
S arcoidosis is a disease with world-wide prevalence that affects all races, ethnic
groups, individuals of all ages, and both sexes. The disease may affect any organ. Its
severity may range from a radiographic or laboratory abnormality detected in a patient
with no symptoms to a relentlessly progressive disease that is potentially life threaten-
ing. Despite the awareness of sarcoidosis as a specifi c disease entity for nearly one
and one-half centuries, there is still no standard method of diagnosis, treatment
approach, method of follow-up evaluation, or method to reliably predict prognosis.
B ecause sarcoidosis is a relatively rare disease, few clinicians have extensive
clinical experience in its management. Furthermore, medical evidence concerning
the clinical approach to sarcoidosis is scarce. Therefore, clinicians typically lack the
necessary tools to make reliable treatment decisions concerning sarcoidosis patients.
T he lung is the most common organ involved with sarcoidosis. Pulmonary mani-
festations of sarcoidosis include asymptomatic radiographic abnormalities, granu-
lomatous infl ammation of airways, and/or the lung interstitium causing pulmonary
symptoms and fi brocystic disease that may result in severe pulmonary dysfunction
and pulmonary hypertension.
T his book will serve as a valuable resource for clinicians concerning the care of
the pulmonary sarcoidosis patient. The focus of this book concerns issues of diag-
nosis, management, and prognosis of the disease. The authors are all clinicians with
extensive experience in caring for these patients. Although they drew on their own
expertise, the authors were encouraged to focus on the clinical data that are avail-
able. I hope that this book will serve as a practical guide for clinicians and thus
improve the care of sarcoidosis patients.
A lbany, N Y, USA M arc A . J udson, M.D.
vii
A cknowledgments
I would like to acknowledge several individuals who were essential in the
production of this book. I would like to thank the major effort of all the authors in
writing these scholarly and clinically relevant chapters. I thank Springer, and in
particular, Ms. Amanda Quinn and Mr. Michael Wilt, whose efforts were essential
in the publication of this work. I thank all of my mentors, colleagues, and mentees
who constantly educated me and questioned me over the years and helped me
develop my passion for learning. In particular, I would like to thank Dr. Steven A.
Sahn for his guidance concerning my academic career and writing skills. I would
like to acknowledge all the sarcoidosis patients who I have treated over the years for
their courage and their kindness. Finally, I thank my parents, my wife, and my chil-
dren for their support and love.
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